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DeCS
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Descriptor English:
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Ichthyosis, Lamellar
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Descriptor Spanish:
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Ictiosis Lamelar
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Descriptor Portuguese:
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Ictiose Lamelar
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Synonyms English:
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Erythroderma Ichthyosiforme, Nonbullous
Ichthyosiform Erythroderma, Nonbullous Congenital
Harlequin Fetus
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Tree Number:
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C16.131.831.512.400.410
C16.320.850.400.410
C16.614.492.400.410
C17.800.428.333.250.410
C17.800.804.512.400.410
C17.800.827.400.410
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Definition English:
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A chronic, congenital ichthyosis inherited as an autosomal recessive trait. Infants are usually born encased in a collodion membrane which sheds within a few weeks. Scaling is generalized and marked with grayish-brown quadrilateral scales, adherent at their centers and free at the edges. In some cases, scales are so thick that they resemble armored plate. |
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Indexing Annotation English:
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do not coord with INFANT, NEWBORN, DISEASES
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History Note English:
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1993; use ICHTHYOSIFORM ERYTHRODERMA, CONGENITAL 1991-1992; ERYTHRODERMA ICHTHYOSIFORME, NONBULLOUS use ICHTHYOSIFORM ERYTHRODERMA, CONGENITAL 1991-1992, use ICHTHYOSIS 1979-1990
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Allowable Qualifiers English:
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Record Number:
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30690
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Unique Identifier:
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D017490
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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